CLINICAL-INSTRUMENTAL PICTURE OF «MORNING GLORY SYNDROME»
Abstract
«Morning glory syndrome» (MGS) is a rare congenital pathology of unknown etiology, which manifests in childhood. In the literature MGS is often described in combination with various ophthalmological anomalies and other diseases, as well as a single pathology.The paper describes 3 clinical MGS cases with a classical fundus picture: a funnel-shaped disc with whitish glial tissue in thecenter and a pigment rim around the disc, macular displacement and abnormal retinal vessels.Additional examination of orbits and brain with the help of MRI revealed deformation of the posterior parts of the eyeball in the optic nerve disk region as a hernial protrusion 0.3 x 0.3x0.3 cm in size. The results of the study indicate that MGS is often a unilateral pathology. Active dynamic observation was recommended for all patients. Any difficulties in making the correct diagnosis require the referral of such patients to specialized ophthalmologic clinics.
Keywords
синдром вьюнка,
аномалия диска зрительного нерва (ДЗН),
оптическая когерентная томография,
флуоресцентная ангиография сетчатки,
магниторезонансная томография,
morning glory syndrome,
optic disk abnormality,
optical coherence tomography,
fluorescent retinal angiography,
magnetic resonance imaging
About the Authors
A. V. Yukhananova
ФГАУ «МНТК «Микрохирургия глаза» им. акад. С.Н. Фёдорова» Минздрава России
Russian Federation
Russian Federation
A. A. Yarovoy
ФГАУ «МНТК «Микрохирургия глаза» им. акад. С.Н. Фёдорова» Минздрава России
Russian Federation
Russian Federation
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Review
For citations:
Yukhananova A.V., Yarovoy A.A. CLINICAL-INSTRUMENTAL PICTURE OF «MORNING GLORY SYNDROME». Bashkortostan Medical Journal. 2018;13(1):48-51. (In Russ.)
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