RARE VULVAR TUMORS BASED ON MATERIALSOF THE REPUBLICAN CLINICAL ONCOLOGY CENTER OF THE REPUBLIC OF BASHKORTOSTAN

Malignant tumors of the vulva are quite rare. In the Russian Federation in 2018, a total of 2068 patients with malignant neoplasms of the vulva were identified, the peak incidence rate is 75-79 years. The specific gravity was 0.61%. Squamous invasive vulvar cancer accounts for more than 90% of all malignant neoplasms of the female external genital organs. Less than 10% of all malignant tumors of the external genitalia in women are accounted for by such nosologies as melanoma, sarcoma, cancer from Merkel cells, and Bartholin cancer.The aim of the study was to analyze rare vulvar tumors based on the materials of the Republican Clinical Oncology Center of the Republic of Bashkortostan.On the basis of the VIII surgical department of the Republican Clinical Oncology Center of the Ministry of Health of the Republic of Bashkortostan for 5 years (2015 - 2019), 192 patients with malignant tumors of the female external genital organs receivedsurgical treatment. According to our data, 15 patients with vulvar cancer have 1 patient with a rare tumor.All patients underwent surgical, combined or complex treatment in the Republican Clinical Oncology Center. The survival rate of this group of patients depends on the type of tumor, its prevalence and adequate surgical and chemoradiotherapy.

vulvar cancer, melanoma, vulvar sarcoma, adenocarcinoma, vulvectomy, inguinal-femoral lymphadenectomy

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